2013-10-07

Last 12 months - Genetics Home Reference

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September 2, 2013

Condition: anhidrotic ectodermal dysplasia with immune deficiency

Gene: IDH2: isocitrate dehydrogenase 2 (NADP+), mitochondrial

Gene: NFKBIA: nuclear factor of kappa light polypeptide gene enhancer in B-cells inhibitor, alpha

Gene: SLC25A1: solute carrier family 25 (mitochondrial carrier; citrate transporter), member 1

Gene family: ANKRD

Gene family: ZC2HC

August 26, 2013

Condition: lissencephaly with cerebellar hypoplasia

Condition: mandibuloacral dysplasia

Condition: nonsyndromic aplasia cutis congenita

Condition: Sjögren syndrome

Gene: RELN: reelin

Gene: ZMPSTE24: zinc metallopeptidase STE24

Gene family: intermediate filaments type V, lamins

August 20, 2013

Condition: complete LCAT deficiency

Condition: familial isolated pituitary adenoma

Condition: fish-eye disease

Condition: isolated Pierre Robin sequence

Condition: late-infantile neuronal ceroid lipofuscinosis

Condition: RAPADILINO syndrome

Gene: AIP: aryl hydrocarbon receptor interacting protein

Gene: CLN5: ceroid-lipofuscinosis, neuronal 5

Gene: CLN6: ceroid-lipofuscinosis, neuronal 6, late infantile, variant

Gene: CLN8: ceroid-lipofuscinosis, neuronal 8 (epilepsy, progressive with mental retardation)

Gene: LCAT: lecithin-cholesterol acyltransferase

Gene: MFSD8: major facilitator superfamily domain containing 8

Gene: TPP1: tripeptidyl peptidase I

August 12, 2013

Condition: sick sinus syndrome

Condition: Snyder-Robinson syndrome

Gene: HCN4: hyperpolarization activated cyclic nucleotide-gated potassium channel 4

Gene: MYH6: myosin, heavy chain 6, cardiac muscle, alpha

Gene: SMS: spermine synthase

Gene family: CNG

August 5, 2013

Condition: Mabry syndrome

Condition: osteoglophonic dysplasia

Condition: Walker-Warburg syndrome

Gene: CDKN1B: cyclin-dependent kinase inhibitor 1B (p27, Kip1)

Gene: FKRP: fukutin related protein

Gene: ISPD: isoprenoid synthase domain containing

Gene: LARGE: like-glycosyltransferase

Gene: PGAP2: post-GPI attachment to proteins 2

Gene: PIGO: phosphatidylinositol glycan anchor biosynthesis, class O

Gene: PIGV: phosphatidylinositol glycan anchor biosynthesis, class V

Gene: POMT1: protein-O-mannosyltransferase 1

Gene: POMT2: protein-O-mannosyltransferase 2

Gene family: dolichyl D-mannosyl phosphate dependent mannosyltransferases

Gene family: PIG

Gene family: glycosyltransferase family 8 domain containing

July 29, 2013

Condition: granulomatosis with polyangiitis

Condition: infantile neuronal ceroid lipofuscinosis

Gene: HLA-DPB1: major histocompatibility complex, class II, DP beta 1

Gene family: immunoglobulin superfamily, C1-set domain containing

July 22, 2013

Condition: Graves disease

Condition: Hashimoto thyroiditis

Condition: retroperitoneal fibrosis

Gene family: WDR

July 15, 2013

Condition: congenital neuronal ceroid lipofuscinosis

Condition: isolated lissencephaly sequence

Gene: CTSD: cathepsin D

Gene: TUBA1A: tubulin, alpha 1a

Gene family: TUB

July 8, 2013

Condition: 8p11 myeloproliferative syndrome

Gene: ZMYM2: zinc finger, MYM-type 2

Gene family: immunoglobulin superfamily, I-set domain containing

Gene family: ZMYM

July 1, 2013

Gene family: CLCN

June 24, 2013

Condition: lacrimo-auriculo-dento-digital syndrome

Gene: FGF10: fibroblast growth factor 10

June 17, 2013

Condition: medullary cystic kidney disease type 1

Condition: Pol III-related leukodystrophy

Gene: MUC1: mucin 1, cell surface associated

Gene: POLR3A: polymerase (RNA) III (DNA directed) polypeptide A, 155kDa

Gene: POLR3B: polymerase (RNA) III (DNA directed) polypeptide B

Gene family: MUC

Gene family: POLR

June 10, 2013

Condition: antiphospholipid syndrome

June 3, 2013

What does it mean to have a genetic predisposition to a disease?

May 29, 2013

Condition: benign chronic pemphigus

Condition: critical congenital heart disease

Condition: Naegeli-Franceschetti-Jadassohn syndrome/dermatopathia pigmentosa reticularis (often shortened to NFJS/DPR)

Condition: Partington syndrome

Condition: renal tubular dysgenesis

Condition: Weaver syndrome

Gene: ACE: angiotensin I converting enzyme

Gene: AGT: angiotensinogen (serpin peptidase inhibitor, clade A, member 8)

Gene: AGTR1: angiotensin II receptor, type 1

Gene: ATP2C1: ATPase, Ca++ transporting, type 2C, member 1

Gene: EZH2: enhancer of zeste homolog 2 (Drosophila)

Gene family: endogenous ligands

May 20, 2013

Condition: Coffin-Siris syndrome

Condition: DICER1 syndrome

Condition: factor V deficiency

Condition: Mainzer-Saldino syndrome

Condition: Pearson marrow-pancreas syndrome

Condition: sitosterolemia

Gene: ABCG5: ATP-binding cassette, sub-family G (WHITE), member 5

Gene: ABCG8: ATP-binding cassette, sub-family G (WHITE), member 8

Gene: ARID1A: AT rich interactive domain 1A (SWI-like)

Gene: ARID1B: AT rich interactive domain 1B (SWI1-like)

Gene: DICER1: dicer 1, ribonuclease type III

Gene: IFT140: intraflagellar transport 140 homolog (Chlamydomonas)

Gene: SMARCA4: SWI/SNF related, matrix associated, actin dependent regulator of chromatin, subfamily a, member 4

Gene: SMARCB1: SWI/SNF related, matrix associated, actin dependent regulator of chromatin, subfamily b, member 1

Gene: SMARCE1: SWI/SNF related, matrix associated, actin dependent regulator of chromatin, subfamily e, member 1

May 13, 2013

Condition: Carpenter syndrome

Gene: EPCAM: epithelial cell adhesion molecule

Gene: MEGF8: multiple EGF-like-domains 8

Gene: RAB23: RAB23, member RAS oncogene family

May 6, 2013

Condition: Baraitser-Winter syndrome

Gene: ACTB: actin, beta

April 29, 2013

Condition: progressive pseudorheumatoid dysplasia

Gene: WISP3: WNT1 inducible signaling pathway protein 3

April 16, 2013

Condition: autosomal recessive hypotrichosis

Condition: Caffey disease

Condition: desmoid tumor

Condition: Horner syndrome

Condition: intrauterine growth restriction, metaphyseal dysplasia, adrenal hypoplasia congenita, and genital anomalies (often shortened to IMAGe syndrome)

Condition: multiple sclerosis

Condition: Ohdo syndrome, Maat-Kievit-Brunner type

Gene: HLA-DRB1: major histocompatibility complex, class II, DR beta 1

Gene: IL7R: interleukin 7 receptor

Gene: LIPH: lipase, member H

Gene: LPAR6: lysophosphatidic acid receptor 6

Gene family: fibronectin type III domain containing

April 9, 2013

Condition: Poland syndrome

Condition: type 1 diabetes

March 25, 2013

What is the prognosis of a genetic condition?

Condition: Denys-Drash syndrome

Condition: Frasier syndrome

Gene: BDNF: brain-derived neurotrophic factor

Gene: KANSL1: KAT8 regulatory NSL complex subunit 1

March 18, 2013

Condition: familial pityriasis rubra pilaris

Gene: CARD14: caspase recruitment domain family, member 14

March 4, 2013

Condition: familial hypertrophic cardiomyopathy

Condition: glycogen storage disease type IV

Condition: Liddle syndrome

Condition: mycosis fungoides

Condition: myosin storage myopathy

Condition: Rotor syndrome

Condition: Sézary syndrome

Gene: MYBPC3: myosin binding protein C, cardiac

Gene: SLCO1B1: solute carrier organic anion transporter family, member 1B1

Gene: SLCO1B3: solute carrier organic anion transporter family, member 1B3

Gene: TNNT2: troponin T type 2 (cardiac)

Gene family: myosin superfamily

Gene family: MYBP

February 25, 2013

Condition: Shprintzen-Goldberg syndrome

Gene: SKI: v-ski avian sarcoma viral oncogene homolog

Gene family: SKOR

February 18, 2013

Condition: X-linked thrombocytopenia

February 11, 2013

Condition: PDGFRB-associated chronic eosinophilic leukemia

Condition: piebaldism

Gene: ETV6: ets variant 6

Gene: PDGFRB: platelet-derived growth factor receptor, beta polypeptide

Gene: SLC20A2: solute carrier family 20 (phosphate transporter), member 2

February 4, 2013

Condition: arterial tortuosity syndrome

Condition: auriculo-condylar syndrome

Condition: genitopatellar syndrome

Condition: MPV17-related hepatocerebral mitochondrial DNA depletion syndrome

Condition: Ohdo syndrome, Say-Barber-Biesecker-Young-Simpson variant (often shortened to Ohdo syndrome, SBBYS variant)

Gene: GNAI3: guanine nucleotide binding protein (G protein), alpha inhibiting activity polypeptide 3

Gene: KAT6B: K(lysine) acetyltransferase 6B

Gene: MPV17: MpV17 mitochondrial inner membrane protein

Gene: PLCB4: phospholipase C, beta 4

Gene: SLC2A10: solute carrier family 2 (facilitated glucose transporter), member 10

Gene family: chromatin-modifying enzymes

January 28, 2013

Condition: combined malonic and methylmalonic aciduria (often shortened to CMAMMA)

Gene: ACSF3: acyl-CoA synthetase family member 3

Gene family: ACS

January 17, 2013

Condition: Myhre syndrome

January 7, 2013

Condition: Cantú syndrome

Condition: juvenile primary osteoporosis

Condition: osteoporosis-pseudoglioma syndrome

Condition: spinal muscular atrophy with respiratory distress type 1 (often shortened to SMARD1)

Gene: ABCC9: ATP-binding cassette, sub-family C (CFTR/MRP), member 9

Gene: DYNC1H1: dynein, cytoplasmic 1, heavy chain 1

Gene family: DYN

December 17, 2012

Condition: Floating-Harbor syndrome

Condition: hereditary diffuse leukoencephalopathy with spheroids (often shortened to HDLS)

Gene: CSF1R: colony stimulating factor 1 receptor

Gene: SRCAP: Snf2-related CREBBP activator protein

December 11, 2012

What is the epigenome?

How are genetic conditions diagnosed?

How are genetic conditions treated or managed?

What is genetic ancestry testing?

What advances are being made in DNA sequencing?

Condition: Lujan syndrome

Condition: task-specific focal dystonia

Condition: Weyers acrofacial dysostosis

December 2, 2012

Condition: Bart-Pumphrey syndrome

Condition: congenital insensitivity to pain

Condition: Dowling-Degos disease

Condition: hereditary sensory and autonomic neuropathy type IE

Condition: hystrix-like ichthyosis with deafness

Condition: keratitis-ichthyosis-deafness syndrome

Condition: palmoplantar keratoderma with deafness

Condition: paroxysmal extreme pain disorder

Condition: small fiber neuropathy

Condition: Vohwinkel syndrome

Gene: DNMT1: DNA (cytosine-5-)-methyltransferase 1

Gene: LOR: loricrin

Gene: SCN10A: sodium channel, voltage-gated, type X, alpha subunit

November 19, 2012

Condition: congenital deafness with labyrinthine aplasia, microtia, and microdontia (often shortened to LAMM syndrome)

Condition: familial HDL deficiency

Gene: APOA1: apolipoprotein A-I

Gene: FGF3: fibroblast growth factor 3

November 5, 2012

Condition: Bietti crystalline dystrophy

Condition: Potocki-Shaffer syndrome

Condition: primary spontaneous pneumothorax

Gene: CYP4V2: cytochrome P450, family 4, subfamily V, polypeptide 2

October 30, 2012

Condition: hypermanganesemia with dystonia, polycythemia, and cirrhosis (often shortened to HMDPC)

Gene: SLC30A10: solute carrier family 30, member 10

October 23, 2012

Condition: adenine phosphoribosyltransferase deficiency

Condition: CHST3-related skeletal dysplasia

Condition: cytochrome c oxidase deficiency

Condition: fatty acid hydroxylase-associated neurodegeneration

Condition: hereditary pancreatitis

Condition: maternally inherited diabetes and deafness (often shortened to MIDD)

Condition: 1q21.1 microdeletion

Gene: APRT: adenine phosphoribosyltransferase

Gene: CHST3: carbohydrate (chondroitin 6) sulfotransferase 3

Gene: FA2H: fatty acid 2-hydroxylase

Gene: MT-TE: mitochondrially encoded tRNA glutamic acid

Gene: PRSS1: protease, serine, 1 (trypsin 1)

Gene family: PRSS

Gene family: SULTM

Gene family: TRNA

October 15, 2012

Condition: familial osteochondritis dissecans

Condition: ulcerative colitis

Gene: ACAN: aggrecan

October 8, 2012

Gene: RBM8A: RNA binding motif protein 8A

October 2, 2012

Condition: glycogen storage disease type IX

Gene: KLLN: killin, p53-regulated DNA replication inhibitor

Gene: PHKA1: phosphorylase kinase, alpha 1 (muscle)

Gene: PHKA2: phosphorylase kinase, alpha 2 (liver)

Gene: PHKB: phosphorylase kinase, beta

Gene: PHKG2: phosphorylase kinase, gamma 2 (testis)

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